Gorham disease: correlation of MR findings with histopathologic changes

Eur Radiol. 1998;8(9):1647-50. doi: 10.1007/s003300050603.

Abstract

Gorham disease is a rare disorder of unknown etiology characterized by bone destruction and abnormal proliferation of thin-walled vascular channels including lymphatic capillaries. Starting monocentrically in a single bone, the angiomatous masses in this disease extend to adjacent bones and soft tissues without respecting articular barriers. Herein we report a case of Gorham disease with its MR and histopathologic appearance.

Publication types

  • Case Reports

MeSH terms

  • Bone Marrow / blood supply
  • Bone Marrow / pathology
  • Connective Tissue / pathology
  • Humans
  • Humerus / pathology
  • Joint Diseases / diagnosis*
  • Joint Diseases / pathology
  • Lymphatic System / pathology
  • Magnetic Resonance Imaging*
  • Male
  • Middle Aged
  • Neovascularization, Pathologic / diagnosis
  • Neovascularization, Pathologic / pathology
  • Osteolysis, Essential / diagnosis*
  • Osteolysis, Essential / pathology
  • Shoulder Joint / pathology*
  • Synovial Membrane / pathology