Intestinal involvement in Wegener's granulomatosis

J Gastrointestin Liver Dis. 2007 Sep;16(3):329-31.

Abstract

Wegener's granulomatosis is a necrotizing vasculitis that may affect any viscera. Gastrointestinal involvement is rather uncommon. We present a case of Wegener's granulomatosis with multiple small bowel ulcers and a single ileal perforation. Histological examination of the surgically resected specimen demonstrated evidence for necrotizing vasculitis. Gross and histological features of the gastrointestinal disease in Wegener's granulomatosis are discussed.

Publication types

  • Case Reports

MeSH terms

  • Adrenal Cortex Hormones / administration & dosage
  • Adrenal Cortex Hormones / therapeutic use
  • Adult
  • Biopsy
  • Emergencies
  • Follow-Up Studies
  • Granulomatosis with Polyangiitis / complications*
  • Granulomatosis with Polyangiitis / diagnosis
  • Granulomatosis with Polyangiitis / diagnostic imaging
  • Granulomatosis with Polyangiitis / drug therapy
  • Granulomatosis with Polyangiitis / pathology
  • Granulomatosis with Polyangiitis / surgery
  • Humans
  • Ileal Diseases / diagnosis
  • Ileal Diseases / diagnostic imaging
  • Ileal Diseases / etiology*
  • Ileal Diseases / pathology
  • Ileal Diseases / surgery
  • Ileum / pathology
  • Immunohistochemistry
  • Intestinal Perforation / diagnosis
  • Intestinal Perforation / diagnostic imaging
  • Intestinal Perforation / etiology*
  • Intestinal Perforation / pathology
  • Intestinal Perforation / surgery
  • Laparotomy
  • Male
  • Radiography, Abdominal
  • Time Factors
  • Tomography, X-Ray Computed
  • Ulcer / pathology
  • Ulcer / surgery

Substances

  • Adrenal Cortex Hormones