Familial granulomatous arthritis, iritis, and rash

doi:10.1016/S0022-3476(85)80394-2

The Journal of Pediatrics

Volume 107, Issue 5, November 1985, Pages 689-693

https://doi.org/10.1016/S0022-3476(85)80394-2 Get rights and content

Eleven family members over four generations have had granulomatous disease of the skin, eyes, and joints. Ten have had arthritis; two had skin, eye, and joint involvement; one had skin and joint disease, and one had iritis only. The disease is transmitted as an autosomal dominant trait and is not associated with HLA-B27. The disease resembles sarcoidosis in some ways but not in ashear, and is probably a new syndrome. The major long-term problems are iritis and joint contractures.

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Original articleFamilial granulomatous arthritis, iritis, and rash

Prognosis of sarcoidosis

Ann Intern Med

Sarcoidosis in young children

Am J Dis Child

Familial granulomatous arteritis with polyarthritis of juvenile onset

N Engl J Med

Familial sarcoidosis with multiple occurences in eleven families: a possible mechanism of inheritance

Ann NY Acad Sci

Original article
Familial granulomatous arthritis, iritis, and rash