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Pulmonary Manifestations of Sjögren’s Syndrome

  • AUTOIMMUNITY (TK TARRANT, SECTION EDITOR)
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Abstract

Sjögren’s syndrome (SS) is primarily defined by its impact on the oral and ocular system resulting in xerostomia and xerophthalmia. However, SS can also manifest throughout the respiratory system. Subclinical pulmonary involvement is common. Clinically significant involvement can result in a 4-fold increased risk of death. Thus, recognizing the many potential presentations of SS in the lung is critical in caring for patients with SS. Additionally, SS should be included in the differential diagnosis of a number of forms of interstitial lung disease.

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Acknowledgments

This work was supported by T32 grant to GS and Fisher Foundation Fund for PF to SD.

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Conflict of Interest

George Stojan declares that he has no conflict of interest.

Alan N. Baer declares that he has no conflict of interest.

Sonye K. Danoff declares that she has no conflict of interest.

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This article does not contain any studies with human or animal subjects performed by any of the authors.

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Authors and Affiliations

  1. Division of Rheumatology, Johns Hopkins University School of Medicine, Baltimore, MD, USA

    George Stojan & Alan N. Baer

  2. Division of Pulmonary Medicine and Critical Care, Department of Medicine, Johns Hopkins University School of Medicine, 1830 Monument Street, 5th floor, Baltimore, MD, 21287, USA

    Sonye K. Danoff

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  1. George Stojan
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Stojan, G., Baer, A.N. & Danoff, S.K. Pulmonary Manifestations of Sjögren’s Syndrome. Curr Allergy Asthma Rep 13, 354–360 (2013). https://doi.org/10.1007/s11882-013-0357-9

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