Table 2.

Study population baseline cardiopulmonary measurements.

MeasurementTotal, n = 88
FVC, % predicted ± SD85.2 ± 21.0
DLCO, % predicted ± SD63.7 ± 20.9
FVC(%)/DLCO(%) ± SD1.4 ± 0.5
6-MWT distance, m ± SD442 ± 103
Resting RVSP, mmHg ± SD32 ± 7
  • FVC: forced vital capacity; 6-MWT: 6-minute walk test; RVSP: right ventricular systolic pressure.