Table 1.

Variables falling in the third quartile, considering the total score obtained for familial Mediterranean fever (FMF).

RankVariableScoreFrequency of CitationMean Score
1Positive genetic analysis for MEFV gene626847.5
2Response to colchicine^ *568876.5
3Increase of acute-phase reactants and serum amyloid A during fever episodes* °471776.1
4Abdominal pain* ° §466845.5
5Ethnicity (Turkish, Arabs, Armenian, Kurds, Jewish) * §426666.5
6Classic recurrent fever pattern^ * °378468.2
7Duration of attacks 1–3 days* °313427.5
8Positive family history^ * °253515.0
9Serositis^ *220366.1
10Erysipeloid rash^198474.2
11Self-limiting episodes*181355.2
12Duration of attacks few hours to 3–4 days* °166227.5
13Chest pain* ° §152354.3
14Arthritis* °127324.0
15Well-being between episodes*124323.9
16Amyloidosis^104205.2
17Increase of acute-phase reactants and serum amyloid A during fever episodes and sometimes between episodes100175.9
18Arthralgia80243.3
  • * Variable already present in Livneh criteria.

  • ^ Tel Hashomer criteria.

  • ° Pediatric FMF criteria.

  • § Preliminary Eurofever criteria.