Table 1.

Systemic manifestation score.

Clinical manifestationPoints
Fever
  37–38°C1
  38–39°C2
  39–40°C3
  > 40°C4
Evanescent erythematous rash1
Generalized lymphadenopathy1
Hepatomegaly and/or splenomegaly1
Serositis1
Anemia (hemoglobin < 9 g/dl)1
Platelet count > 600 × 109/l or ferritin > 500 ng/ml1