Variables | n = 27 |
---|---|
Center, Nice/Lille | 18/9 |
Sex, female/male | 24/3 |
Age, yrs, median (range) | 59 (38–81) |
BMI, kg/m2, median (IQR) | 25 (22–28) |
History of smoking | 9 |
NYHA score | |
Class I | 3 |
Class II | 13 |
Class III | 8 |
Class IV | 3 |
lcSSc/dcSSc | 22/5 |
Overlap syndromes | 5 |
Antibodies | |
Anticentromere | 9 |
Antitopoisomerase I | 11 |
Other | 10 |
Disease ≥ 5 yrs | 16 |
Modified Rodnan score, median (IQR) | 4.5 (2.0–12) |
Raynaud phenomenon | 26 |
Digital ulcers | 14 |
Telangiectasia | 16 |
Articular expression of the disease | 6 |
Gastroesophageal reflux disease | 17 |
Arterial hypertension | 7 |
History of SSc renal crisis | 0 |
Preexisting signs of right heart disease | 3 |
ECG conduction blocks | 8 |
Dry cough | 8 |
Hemoglobin, g/dl (IQR) | 12.40 (12.08–13.73) |
Creatinine, µmol/l (IQR) | 71 (61–82) |
BNP < 50 ng/l or NT-proBNP < 300 ng/l | 15 |
BNP 50–300 ng/l or NT-proBNP 300–1400 ng/l | 8 |
BNP > 300 ng/l or NT-proBNP > 1400 ng/l | 0 |
BMI: body mass index; IQR: interquartile range; NYHA: New York Heart Association; SSc: systemic sclerosis; lcSSc: limited cutaneous SSc; dcSSc: diffuse cutaneous SSc; BNP: brain natriuretic peptide; ECG: electrocardiograph; NT-proBNP: N terminal proBNP.