Table 2.

No. patients who met FMF diagnosis in our series according to different diagnostic tools. Data are n/N (%).

Yalcinkaya-Ozen CriteriaTel Hashomer CriteriaLivneh Criteria
FMF patients positive for FMF250/286 (87.4)122/271 (45.0)221/286 (77.3)
CAPS false-positive for FMF10/32 (31.3)0/32 (0.0)12/32 (37.5)
MKD false-positive for FMF25/45 (55.6)2/45 (4.4)35/45 (77.8)
TRAPS false-positive for FMF30/53 (56.6)3/53 (5.7)42/53 (79.2)
PFAPA false-positive for FMF53/160 (33.1)2/160 (1.1)62/160 (38.8)
Undefined patients38/87 (43.7)1/87 (1.1)53/87 (60.9)
  • FMF: familial Mediterranean fever; CAPS: cryopyrin-associated periodic syndrome; MKD: mevalonate kinase deficiency; TRAPS: tumor necrosis factor receptor–associated periodic syndrome; PFAPA: aphthous stomatitis, pharyngitis, adenitis syndrome.