Total Patients with SSc | 2013 ACR/EULAR Criteria | Total N (%) | ||
---|---|---|---|---|
n < 9 points (%) | n ≥ 9 points (%) | |||
1980 ARA criteria | Not fulfilled | 118 (27.8) | 290 (68.4) | 408 (100) (34.6) |
Fulfilled | 7 (0.9) | 742 (98.1) | 749 (100) (63.5) | |
Total | 125 (13.5) | 1032 (87.5) | 1157 (100) | |
Patients with lcSSc | 2013 ACR/EULAR Criteria | Total | ||
n < 9 points (%) | n ≥ 9 points (%) | N (%) | ||
1980 ARA criteria | Not fulfilled | 8 (3.2) | 244 (96.8) | 252 (100) (37) |
Fulfilled | 2 (0.5) | 427 (99.5) | 429 (100) (63) | |
Total | 10 (1.5) | 671 (98.5) | 681 (100) | |
Patients with dcSSc | 2013 ACR/EULAR Criteria | Total | ||
n < 9 points (%) | n ≥ 9 points (%) | N (%) | ||
1980 ARA criteria | Not fulfilled | 0 (0) | 0 (0) | 0 (0) |
Fulfilled | 0 (0) | 309 (100) | 309 (100) | |
Total | 0 | 309 (100) | 309 | |
Patients with ss-SSc | 2013 ACR/EULAR Criteria | Total | ||
n < 9 points (%) | n ≥ 9 points (%) | N (%) | ||
1980 ARA criteria | Not fulfilled | 52 (59.8) | 35 (40.2) | 87 (100) (88.8) |
Fulfilled | 5 (45.5) | 6 (54.5) | 11 (100) (11.2) | |
Total | 57 (58.2) | 41 (41.8) | 98 | |
Pre-SSc patients | 2013 ACR/EULAR Criteria | Total | ||
n < 9 points (%) | n ≥ 9 points (%) | N (%) | ||
1980 ARA criteria | Not fulfilled | 58 (84.1) | 11 (15.9) | 69 (100) |
Fulfilled | 0 (0) | 0 (0) | 0 (0) | |
Total | 0 | 11 (15.9) | 69 |
SSc: systemic sclerosis; lcSSc: limited cutaneous SSc; dcSSc: diffuse cutaneous SSc; ss-SSc: sine scleroderma SSc; ACR/EULAR: American College of Rheumatology/European League Against Rheumatism; ARA: American Rheumatism Association.