Table 1.

Clinical and demographic features of the 10 patients with diffuse SSc.

Sex/Age, YrsYr of SSc Onset/Disease Duration at Skin Biopsy, YrsmRSS/Score at Skin BiopsyAutoantibodiesLung Involvement from HRCT/PFTHeart Involvement/Scleroderma Renal CrisisRaynaud Phenomenon/Digital Ulcers
F/462010/212/2ANA/Scl-70Normal/NormalNormal/NoYes/No
F/212009/313/1ANA/Scl-70Normal/NormalNormal/NoYes/Yes
F/312011/113/2ANA/Scl-70Normal/NormalNormal/NoYes/Yes
F/362010/211/2ANA/Scl-70Normal/NormalPAH/NoYes/Yes
M/202010/211/1ANA/Scl-70Normal/NormalNormal/NoYes/No
F/412010/215/2ANA/Scl-70Normal/NormalNormal/NoNo/No
F/302010/210/1ANA/Scl-70Normal/NormalNormal/NoYes/No
F/212010/209/1ANA/Scl-70Normal/NormalNormal/NoYes/No
F/312009/314/1ANA/Scl-70Normal/NormalNormal/NoYes/No
F/422009/316/2ANA/Scl-70Fibrosis/NormalNormal/NoYes/No
  • SSc: systemic sclerosis; mRSS: modified Rodnan skin score, maximum possible score 51; HRCT: high-resolution computed tomography; PFT: pulmonary function test; ANA: antinuclear antibodies; Scl-70: antitopoisomerase; PAH: pulmonary arterial hypertension.