Table 2.

SIR of malignancies in IgG4-RD and AIP.

IgG4-RDAIP
SIR95% CISIR95% CI
Overall2.011.34–2.692.081.32–2.85
Without concurrent diagnosis1.601.07–2.131.711.01–2.41
Years after IgG4-RD diagnosis
  < 13.531.23–5.833.911.02–6.80
  ≥ 11.480.99–1.981.570.90–2.23
  • SIR: standardized incidence ratio; IgG4-RD: immunoglobulin G4–related disease; AIP: autoimmune pancreatitis.