Conditions documented for patients with at least 1 IF-negative, MPO/PR3-positive result, and without a diagnosis of AAV.
| Age, yrs | Sex | MPO, n | PR3, n | Condition |
|---|---|---|---|---|
| 40 | M | 0 | 63 | Demyelinating polyneuropathy |
| 51 | M | 2 | 59 | Hashimoto thyroiditis, chronic sinusitis |
| 45 | F | 0 | 47 | Cocaine use |
| 20 | M | 0 | 37 | Henoch-Schönlein purpura |
| 42 | F | 1 | 35 | Cutaneous papulonodular eruption with lymphocytic vasculitis |
| 86 | F | 0 | 33 | Pyoderma gangrenosum, COPD |
| 63 | F | 3 | 31 | SLE, breast cancer |
| 20 | F | 0 | 30 | IBD |
| 47 | F | 1 | 29 | Graft versus host disease |
| 61 | M | 0 | 29 | IBD |
| 73 | M | 0 | 27 | COPD, breast cancer |
| 79 | F | 0 | 26 | IBD, hydralazine exposure |
| 54 | M | 0 | 26 | Hepatitis C, hepatocellular carcinoma |
| 23 | F | 121 | 2 | SLE, autoimmune polyneuropathy |
| 19 | M | 116 | 1 | Retiform purpura* |
| 92 | F | 79 | 0 | Bronchiectasis, breast cancer |
| 22 | F | 64 | 6 | SLE, cutaneous vasculitis |
| 50 | F | 63 | 1 | Goodpasture disease |
| 33 | F | 53 | 1 | AS, drug-induced SLE |
| 28 | F | 50 | 2 | SLE |
| 65 | F | 45 | 0 | RA, idiopathic progressive polyneuropathy |
| 23 | M | 38 | 2 | SLE |
| 49 | M | 36 | 5 | Desquamative interstitial pneumonia |
| 79 | F | 36 | 0 | COPD |
| 72 | F | 31 | 0 | Hypoaldosteronism, sinusitis |
| 51 | F | 29 | 1 | Relapsing polychondritis, leukocytoclastic vasculitis |
↵* Lost to followup before investigations completed. IF: immunofluorescence; MPO: myeloperoxidase; PR3: proteinase 3; AAV: ANCA-associated vasculitis; COPD: chronic obstructive pulmonary disease; SLE: systemic lupus erythematosus; IBD: inflammatory bowel disease; AS: ankylosing spondylitis; RA: rheumatoid arthritis; ANCA: antineutrophil cytoplasmic antibodies.