Table 3.

Overview of the 2013 ACR/EULAR classification criteria items in the Oslo University Hospital SSc cohort (N = 425), and in the nationwide MCTD cohort (N = 178).

Items (points)SSc (N = 425), n/N Tested (%)MCTD (N = 178), n/N Tested (%)
Bilateral skin thickening proximal to the MCP joints (9)97/425 (23)0
Skin thickening of the fingers; whole finger distal to MCP (4), puffy fingers (2)294/425 (69)146/178 (82)
Finger tip lesions; digital ulcers (2), or pitting scars (3)169/419 (40)12/147 (8)
Telangiectasia (2)283/408 (69)NA
Abnormal nailfold capillaries (2)292/318 (92)NA
Pulmonary arterial hypertension and/or interstitial lung disease (2)182/407 (45)44/178 (25)
Raynaud phenomenon (3)402/418 (96)176/178 (99)
Scleroderma-related antibodies (3) (ACA, ATA, or anti-RNAP)310/407 (76)4/178 (2)
Total score of 9 or more points409/425 (96)18/178 (10)
  • SSc: systemic sclerosis; MCTD: mixed connective tissue disease; lcSSc: limited cutaneous systemic sclerosis; dcSSc: diffuse cutaneous systemic sclerosis; MCP: metacarpophalangeal; ACA: anticentromere antibody; ATA: antitopoisomerase antibody; anti-RNAP: anti-RNA polymerase antibodies; NA: not applied; ACR: American College of Rheumatology; EULAR: European League Against Rheumatism.