Comparison between the ACR 1980 classification criteria and the ACR/EULAR 2013 criteria in the 3 patients at the onset of retinal vessels occlusion.
| No. | ACR 1980 Classification Criteria* | ACR/EULAR 2013 Classification Criteria‡ | Score |
|---|---|---|---|
| 1 | 1 minor criterion, interstitial lung fibrosis | Raynaud phenomenon | 3 |
| ANA-positive, anticentromeric pattern | 3 | ||
| Early scleroderma pattern, NVC | 2 | ||
| Interstitial lung fibrosis | 2 | ||
| Total 10 | |||
| 2 | 1 minor criterion, sclerodactyly | Raynaud phenomenon | 3 |
| Puffy fingers | — | ||
| Sclerodactyly | 4 | ||
| ANA-positive, anticentromeric pattern | 3 | ||
| Active scleroderma pattern, NVC | 2 | ||
| Total 12 | |||
| 3 | None | Raynaud phenomenon | 3 |
| ANA-positive, anticentromere pattern | 3 | ||
| Pitting scars | 3 | ||
| Active scleroderma pattern, NVC | 2 | ||
| Total 11 |
↵* Patient with 1 major criterion or ≥ 2 minor criteria are classified as having definitive SSc 9.
↵‡ Patients with a total score of ≥ 9 are classified as having definitive SSc10. ACR: American College of Rheumatology; EULAR: European League Against Rheumatism; NVC: nailfold videocapillaroscopy; ANA: anti-nuclear antibodies; SSc: systemic sclerosis.