Age
  Mean ± SD53.0 ± 13.8
  Median (IQR)51.0 (45.0–64.0)
Sex
  Men, n (%)18 (27)
  Women, n (%)48 (73)
Disease duration (in years)
  Mean ± SD5.90 ± 6.52
  Median (IQR)4.50 (1.00–9.00)
Leroy subset, n (%)
  LSSc19 (29)
  LcSSc34 (51)
  DcSSc13 (20)
NVC pattern, n (%)
  Early5 (8)
  Active25 (38)
  Late27 (41)
  Normal — Aspecific changes9 (13)
Antibodies profile, n (%)
  ACA23 (35)
  Anti-topo14 (21)
  Anti-RNA pol III7 (11)
  Pm-Scl0 (0)
  ACA and anti-topo1 (1)
Peripheral vascular therapy, n (%) “yes”
  Prostacyclins13 (20)
  Calcium antagonists24 (36)
  Endothelin receptor antagonists0 (0)
  Phosphodiesterase type 5 inhibitor0 (0)
Pulmonary-vascular therapy0 (0)
  Prostacyclins0
  Endothelin receptor antagonists0
  Phosphodiesterase type 5 inhibitor0
Lost to followup, n8
  Due to logistic reasons4
  Non-SSc-related reasons3
  SSc-related reasons*1
  • * Patient went to another hospital for lung transplantation. NVC: nailfold videocapillaroscopy; IQR: interquartile range; LSSc: limited systemic sclerosis; LcSSc: limited cutaneous systemic sclerosis; DcSSc: diffuse cutaneous systemic sclerosis; ACA: anticentromere antibodies; anti-topo: antitopoisomerase; SSc: systemic sclerosis.