Table 1.

Demographic data and disease subtype in the study cohort. Data are mean (SD) unless otherwise indicated.

CharacteristicTotal Study Cohort, n = 312Survivors, n = 269Deceased, n = 43p
Demographic, n (%)
  Female241 (77)213 (79)28 (65)0.03
  Male71 (33)56 (21)15 (35)
  Age at disease onset*, yrs47 (14.4)46 (14.2)54 (14.3)0.005
  Age at SSc diagnosis, yrs54 (14.5)50 (14.7)57 (13.7)0.043
  Age at death, yrs57 (13.5)56 (13.2)64 (12.1)0.000
  Disease duration**, yrs9.9 (7.4)9.7 (7.5)10.8 (8.1)0.357
  Followup***, yrs8.1 (6.8)8.2 (6.8)8.0 (6.8)0.895
Disease subgroup, n (%)
  Limited35 (11)34 (13)1 (2.3)0.003
  Limited cutaneous209 (67)184 (68)25 (58)
  Diffuse cutaneous68 (22)51 (19)17 (40)
  • * Defined by the first non-Raynaud phenomenon symptom.

  • ** The period between first non-Raynaud phenomenon symptom and study end/death.

  • *** The period between time of diagnosis and study end/death.