Table 2.

Frequency of organ-specific involvement at time of diagnosis in 9 children with eosinophilic granulomatosis with polyangiitis (EGPA).

Organ System%Organ System%
Upper airway100Cutaneous67
  Allergic rhinitis33  Subcutaneous nodules11
  Sinusitis89  Petechiae11
  Nasal polyps33  Ecchymosis33
  Chronic otitis11  Urticaria11
Pulmonary100  Other33
  Asthma89Neurologic56
  Non-fixed infiltrates67  Mononeuritis multiplex33
  Pleural effusion22  Neuropathic pain22
  Alveolar hemorrhage22  Cerebral infarction11
  Lung nodules44Cardiac44
Musculoskeletal67  Pericardial effusion33
  Migratory polyarthralgias33  Dilated cardiomyopathy22
  Arthritis22  Valvular insufficiency33
  Myalgias22  Heart failure22
  Weakness11  Abnormal electrocardiogram22
Gastrointestinal67  Myocardial ischemia11
  Eosinophilic esophagitis22  Myocardial infarction11
  Eosinophilic gastritis22  Abnormal echocardiogram44
  Abdominal pain56Renal0
  Diarrhea33
  Colitis33