Severity score by Pras, et al9 modified for children. The severity score is the sum of the score of each variable. A score of 3–5 is accepted as mild, 6–9 is moderate, and > 9 is severe disease.
| Variable | Score |
|---|---|
| Age at onset, yrs | |
| 11–20 | 2 |
| 3–10 | 3 |
| < 3 | 4 |
| No. attacks per month | |
| < 1 | 1 |
| 1–2 | 2 |
| > 2 | 3 |
| Arthritis | |
| Acute | 2 |
| Protracted | 3 |
| Erysipelas-like erythema | 2 |
| Amyloidosis | 3 |
| Dose of colchicine, mg/m2 | |
| < 1 | 0 |
| 1 | 1 |
| > 1 | 2 |
| > 2 mg/day* | 3 |
↵* Not responsive to 2 mg/day.