Severity score by Mor, et al17 modified for children. Severe disease ≥ 3 criteria; intermediate disease = 2 criteria; mild disease ≤ 1 criterion.
| Score | Criteria |
|---|---|
| 1 | > 1 site in a single attack* |
| 2 | > 2 sites in the course of disease |
| 3 | > 1 mg/m2/day colchicine to achieve remission |
| 4 | ≥ 2 pleuritic attacks during course of the disease |
| 5 | ≥ 2 Erysipelas-like erythema attacks during course of the disease |
| 6 | Age of onset ≤ 10 years. |
↵* In at least 25% of attacks.