Causes of death. Data are number.
| Deaths Related to SSc (n = 110) | |
| Lung involvement | 53 (48.1) |
| Interstitial lung disease (ILD) | 18 (16.3) |
| Pulmonary hypertension (PH) | 18 (16.3) |
| ILD + PH | 17 (15.5) |
| Heart involvement | 27 (24.5) |
| Congestive cardiac failure | 20 (18.2) |
| Cardiac arrhythmia | 7 (6.3) |
| Scleroderma renal crisis | 12 (10.9) |
| Multiorgan failure | 10 (9.2) |
| Gastrointestinal | 5 (4.6) |
| Unknown | 3 (2.7) |
| Deaths Not Related to SSc (n = 58) | |
| Septicemia | 24 (41.4) |
| Sudden death | 12 (20.7) |
| Cardiovascular or cerebrovascular | 8 (13.8) |
| Neoplasia | 8 (13.8) |
| Other | 6 (10.3) |
SSc: systemic sclerosis.