Types of pulmonary hypertension (PH) affecting patients with systemic sclerosis. Adapted from the Dana Point 2009 criteria for PH5.
| Group | Pulmonary Hypertension | Abbreviation |
|---|---|---|
| 1 | Pulmonary arterial hypertension associated with connective tissue diseases | PAH |
| 2 | Pulmonary venous hypertension associated with left heart disease (e.g., diastolic dysfunction) | PVH |
| 3 | Pulmonary hypertension associated with respiratory disease (e.g., pulmonary fibrosis) | PH-ILD |