Demographic status |
Male/female | 103/119 |
Age of onset (yrs), mean ± SD | 5.95 ± 3.43 |
Age at diagnosis (yrs), mean ± SD | 8.38 ± 3.65 |
Delay in diagnosis of FMF (yrs), mean SD | 2.42 ± 2.11 |
Clinical feature |
Abdominal pain | 205 (92.3) |
Fever | 202 (90.9) |
Arthritis | 97 (43.7) |
Chest pain | 43 (19.4) |
Myalgia | 38 (17.1) |
Erysipelas-like erythema | 16 (7.2) |
Protracted febrile myalgia | 3 (1.4) |
Protracted arthritis | 2 (0.9) |
Phenotype II | 2 (0.9) |
Mean severity score | 8.59 ± 1.93 |
Diseases associated with FMF |
Henoch-Schönlein purpura | 9 (4.1) |
Polyarteritis nodosa | 3 (1.4) |
Behçet syndrome | 2 (0.9) |
Inflammatory bowel disease | 1 (0.5) |
Misdiagnosis |
Appendectomy | 22 (10.0) |
Acute rheumatic fever | 10 (4.5) |
Consanguinity | 61 (27.5) |
Family history of FMF | 113 (50.9) |
Family history of amyloidosis | 22 (9.9) |