Table 1.

Clinical conditions of patients with adult-onset Still’s disease (AOSD).

Clinical ConditionsAcute AOSD, n = 22Chronic AOSD n = 6Sepsis, n = 14
Fever20212
Evanescent rash1000
Pharyngitis420
Arthritis2030
Myalgia1030
Pleuritis702
Pericarditis500
Pneumonitis408
Lymphadenopathy311
Hepatomegaly or elevated liver enzymes1102
Leukocyte count > 15,000/μl1405
Ferritin > 3000 μg/l1911
Mean (SD)5.56 (1.67)1.17 (0.98)2.36 (0.93)
Median5.001.002.00
p< 0.001
p< 0.001