Table 1.

Comparison of different scores for adult-onset Still’s disease.

ManifestationGoldman 19807Cush 19872Calabro 19863Reginato 19879Kahn 19918Yamaguchi 199210Fautrel 200114Crispin 20054*
FeverXXXXXXXXXXXXXXXX
Serological factors
  LeukocytosisXXXXXXXXXXXX18
  Liver dysfunctionXXX
  Negative ANAXXXXXXXXX
  Negative RFXXXXXXX
  FerritinXX
Organ manifestations
  RashXXXXXXXXXXXX5
  Arthralgia/arthritisXXXXXXXXXXXXXX10
  Sore throat/pharyngitisXXXXX7
  Pleuritis/pericarditisXXXX
  SplenomegalyXXXX5
  LymphadenopathyXXXX
  HepatomegalyXX
  Organ involvementX
  MyalgiaXXX
  Similar episode in childhoodXX
  Positive diagnosis5 major, > 1 minor3 major, 2 minor4 major, 2 minor4 major, or fever + arthritis + 1 major + 1 minor4 major or 3 major + 2 minor5 positive criteria, 2 major4 major or 3 major + 2 minor≥ 30 points
  • * Criteria display different values. XX: major criteria; X: minor criteria; ANA: antinuclear antibodies; RF: rheumatoid factor.