Manifestation | Goldman 19807 | Cush 19872 | Calabro 19863 | Reginato 19879 | Kahn 19918 | Yamaguchi 199210 | Fautrel 200114 | Crispin 20054* |
---|---|---|---|---|---|---|---|---|
Fever | XX | XX | XX | XX | XX | XX | XX | XX |
Serological factors | ||||||||
Leukocytosis | XX | X | X | XX | XX | XX | XX | 18 |
Liver dysfunction | X | XX | ||||||
Negative ANA | XX | XX | XX | XX | X | |||
Negative RF | XX | XX | XX | X | ||||
Ferritin | XX | |||||||
Organ manifestations | ||||||||
Rash | X | X | XX | XX | XX | XX | XX | 5 |
Arthralgia/arthritis | XX | XX | XX | XX | XX | XX | XX | 10 |
Sore throat/pharyngitis | X | X | X | XX | 7 | |||
Pleuritis/pericarditis | X | X | X | X | ||||
Splenomegaly | X | X | X | X | 5 | |||
Lymphadenopathy | X | X | X | X | ||||
Hepatomegaly | X | X | ||||||
Organ involvement | X | |||||||
Myalgia | XX | X | ||||||
Similar episode in childhood | XX | |||||||
Positive diagnosis | 5 major, > 1 minor | 3 major, 2 minor | 4 major, 2 minor | 4 major, or fever + arthritis + 1 major + 1 minor | 4 major or 3 major + 2 minor | 5 positive criteria, 2 major | 4 major or 3 major + 2 minor | ≥ 30 points |
↵* Criteria display different values. XX: major criteria; X: minor criteria; ANA: antinuclear antibodies; RF: rheumatoid factor.