Feature | Group A: Minor Extent of Organ Involvement, N = 61 | Cluster B: Major Extent of Organ Involvement, N = 19 | Complete Case Series, N = 80 |
---|---|---|---|
dcSSc | 8 | 79 | 25 |
lcSSc | 92 | 21 | 75 |
Hand involvement | |||
Arthralgias | 44 | 63 | 49 |
Arthritis | 10 | 11 | 10 |
Digital ulcers | 41 | 63 | 46 |
Flexion contractures | 13 | 74 | 28 |
Heart involvement | 10 | 79 | 26 |
Lung involvement | |||
Bibasilar fibrosis | 34 | 95 | 49 |
Pulmonary arterial hypertension | 10 | 63 | 23 |
Esophagus involvement | 62 | 89 | 69 |
dcSSc: diffuse cutaneous systemic sclerosis; lcSSc: limited cutaneous systemic sclerosis.