Pyoderma Gangrenosum-Associated Autoinflammatory Syndrome With Skin Abscesses: Successful Treatment With Anti-Interleukin 1 Therapy

Pyoderma gangrenosum (PG)-associated autoinflammatory syndromes (PGAAIS)^1,2 encompass clinical phenotypes such as pyogenic arthritis, PG, and acne (PAPA) syndrome, and PG, acne, hidradenitis suppurativa (PASH) syndrome.^1-4 However, some patients exhibit features of these syndromes without fitting the current nomenclature.¹