Objective To develop and validate revised classification criteria for granulomatosis with
polyangiitis (GPA). Methods Patients with vasculitis or comparator diseases were recruited into …

Objective To develop and validate revised classification criteria for eosinophilic granulomatosis
with polyangiitis (EGPA). Methods Patients with vasculitis or comparator diseases were …

Objectives To determine the causes of death and risk factors in systemic sclerosis (SSc).
Methods Between 2000 and 2011, we examined the death certificates of all French patients …

Objective To develop and validate classification criteria for microscopic polyangiitis (MPA).
Methods Patients with vasculitis or comparator diseases were recruited into an international …

Objective To develop and validate new classification criteria for Takayasu arteritis (TAK).
Methods Patients with vasculitis or comparator diseases were recruited into an international …

To specify the incidence and risk factors for secondary autoimmune diseases (ADs) after
HSCT for a primary AD, we retrospectively analyzed AD patients treated by HSCT reported to …

OBJECTIVE: To determine the efficacy of the interleukin (IL)-1-receptor antagonist (IL-1RA)
anakinra in patients with adult-onset Still’s disease (AOSD) refractory to standard treatments …

Objective Systemic sclerosis ( SS c) is a heterogeneous connective tissue disease that is
typically subdivided into limited cutaneous SS c (lc SS c) and diffuse cutaneous SS c (dc SS c) …

Introduction: The German PID-NET registry was founded in 2009, serving as the first national
registry of patients with primary immunodeficiencies (PID) in Germany. It is part of the …

Introduction. The mainstay in the treatment of the large-vessel vasculitides giant cell arteritis
(GCA) and Takayasu arteritis (TA) are glucocorticosteroids (GC) for induction of remission …