Abstract
Immunoglobulin G4-related diseases (IgG4-RD) are a newly recognized category of diseases. CNS involvement in IgG4-RD includes hypophysitis(1) and intracranial or spinal manifestations of hypertrophic pachymeningitis.(2,3) We present a unique case of rapid cognitive decline due to IgG4-related leptomeningitis.
MeSH terms
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Aged
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Autoimmune Diseases of the Nervous System / complications
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Autoimmune Diseases of the Nervous System / diagnosis
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Autoimmune Diseases of the Nervous System / immunology*
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Biopsy
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Brain / pathology
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Cognition Disorders / etiology
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Cognition Disorders / immunology*
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Female
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Humans
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Immunoglobulin G / immunology*
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Magnetic Resonance Imaging
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Meninges / pathology
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Meningitis / complications
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Meningitis / diagnosis
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Meningitis / immunology*