Abstract
Common variable immunodeficiency (CVID) is a heterogeneous group of disorders, characterized by decreased serum levels of immunoglobulins and abnormal antibody response to protein and/or polysaccharide antigens, leading to recurrent respiratory and gastrointestinal infections, autoimmunity and malignancies. Meanwhile, several monogenic defects with CVID-like phenotype have been identified during the last decade. There is a need to reach international consensus by modifying criteria for CVID, considering various areas of uncertainty in the field.
MeSH terms
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Antibody Formation
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Common Variable Immunodeficiency / blood*
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Common Variable Immunodeficiency / complications
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Common Variable Immunodeficiency / diagnosis*
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Common Variable Immunodeficiency / immunology
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Gastrointestinal Diseases / blood
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Gastrointestinal Diseases / diagnosis
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Gastrointestinal Diseases / etiology
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Gastrointestinal Diseases / immunology
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Humans
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Immunoglobulins / blood
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Immunoglobulins / immunology
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Neoplasms / blood
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Neoplasms / diagnosis
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Neoplasms / etiology
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Neoplasms / immunology
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Respiratory Tract Infections / blood
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Respiratory Tract Infections / diagnosis
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Respiratory Tract Infections / etiology
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Respiratory Tract Infections / immunology