Early onset sarcoidosis with aortitis--"juvenile systemic granulomatosis?"

J Rheumatol. 1990 Jan;17(1):102-6.

Abstract

A syndrome of granulomatous arthritis-uveitis-rash has been described in children. Since the clinical features of arthritis in this syndrome closely resemble those seen in early onset sarcoidosis, and since large vessel vasculitis has been seen in children with sarcoidosis, it is possible that early onset sarcoidosis and granulomatous arthritis-uveitis-rash syndrome are part of the same clinical spectrum. Clinical features of a child with sarcoidosis and Takayasu arteritis described in this report support this hypothesis.

Publication types

  • Case Reports

MeSH terms

  • Aortic Arch Syndromes / complications*
  • Arthritis / complications
  • Child, Preschool
  • Diagnosis, Differential
  • Female
  • Humans
  • Middle Aged
  • Sarcoidosis / complications*
  • Sarcoidosis / diagnosis
  • Skin Diseases / complications
  • Takayasu Arteritis / complications*
  • Takayasu Arteritis / diagnosis
  • Uveitis / complications
  • Vasculitis / complications