Chest
ReviewsPulmonary Vasculitis in Behçet Disease
Section snippets
Materials and Methods
We conducted a comprehensive review of the literature to analyze cumulated data about pulmonary involvement in BD. The PubMed database was searched for articles using the term BD combined with one of the following terms: pulmonary artery, lung, pulmonary involvement, and pleura. Pertinent articles cited as references in the identified articles also were reviewed. These articles were in English, French, Spanish, Japanese, German, Portuguese, Polish, Italian, Romanian, and Turkish; only articles
Results
Our findings are presented in two parts: PAA and pulmonary parenchymal changes/other problems. The distinction between pulmonary parenchymal changes and other problems is difficult in most of the cases. Since the specificity of pulmonary parenchymal changes/other problems is not clear and in order to avoid repetition, the data are presented in the “Discussion.”
Discussion
The first case with BD-associated pulmonary problems was published in 1959.109 Thereafter, many cases with different pulmonary diseases/problems have been reported. Many of these studies cite case reports published before 1937, the description year of BD. The frequency of pulmonary problems shows a wide variation, from < 1 to 18% (Table 5).123126135136 Pulmonary disorders in BD are one of the most common direct causes of death.145
Although many patients with BD and pulmonary problems have been
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2021, Reumatologia ClinicaCitation Excerpt :Moreover, Edrees and colleagues reported that approximately one-third of their patients with pulmonary disease had concomitant fever.19 In addition, the coexistence of pulmonary aneurysms, vena caval involvement, intracardiac thrombosis and PAD was reported in Israeli18 and Turkish studies.24,25 It could take years for BD to evolve to the point of fulfilment of the classification criteria.
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