Dermatomyositis*
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Cited by (140)
The clinical features of juvenile dermatomyositis: A single-centre inception cohort
2022, Seminars in Arthritis and Rheumatism50 Years Ago in THE JOURNAL OF PEDIATRICS: What Changed the Prognosis of Juvenile Dermatomyositis?
2022, Journal of PediatricsUpdates on Juvenile Dermatomyositis from the Last Decade: Classification to Outcomes
2021, Rheumatic Disease Clinics of North AmericaCitation Excerpt :The high frequency of damage in these cohorts point to the urgent need for better JDM treatments. Although mortality rates for JDM have improved since the 1960s, when it was reported in one-third of patients,117 current rates remain unacceptably high. The JDM specific mortality rate from the National Institutes of Health natural history questionnaire–based protocols administered between 1989 and 2011 was estimated at 2.4%, most commonly attributed to ILD.118
Juvenile Idiopathic Inflammatory Myopathies
2018, Pediatric Clinics of North AmericaJuvenile dermatomyositis: Latest advances
2017, Best Practice and Research: Clinical RheumatologyCitation Excerpt :No difference in the frequency of menstrual disturbances or the development of secondary sexual characteristics has been observed [65]. While overall mortality rate has significantly improved (falling from 30% [66] to less than 2% [41]) since the introduction of corticosteroids, DMARDS and novel biologics, the systemic inflammatory response remains profound in some children with JDM, and for a small subset, the resulting pulmonary, gastrointestinal or multisystem failure is fatal [67]. Risk factors include delay to treatment, older age, severe disease activity at onset and weight loss [67].
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Supported in part by National Institutes of Health Training Grant, United States Public Health Service 2A-5284.
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Department of Pediatrics, University of Texas Medical Center, Galvesion, Texas.
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Address, Department of Pediatrics, University of Texas Medical Branch, Galveston, Texas.