Abstract
Progressive systemic sclerosis (PSS) can involve the skin diffusely or in a limited way. Rarely cutaneous involvement can assume a hypertrophic form, described in the literature as keloidal scleroderma. The authors describe a PSS patient who presented cutaneous manifestations compatible with the diagnosis of this clinical situation. The clinical features, pathogenic mechanism and therapeutic approach are discussed and a broad review of the literature is given.
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Abbreviations
- PSS:
-
Progressive systemic sclerosis
References
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Santiago, M., de Castro, D.O., Costa, C.A. et al. Keloidal scleroderma. Clin Rheumatol 23, 50–51 (2004). https://doi.org/10.1007/s10067-003-0823-1
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DOI: https://doi.org/10.1007/s10067-003-0823-1