Table 1.

Patient characteristics. All patients had severe juvenile idiopathic arthritis–associated uveitis refractory to corticosteroids and systemic immunosuppression (n = 21 patients).

Age, yrs (mean ± SD)*11.8 ± 3.6
Male/female (n)5/16
ILAR classification, n/%
  Persistent oligoarthritis7/33.3
  Extended oligoarthritis9/42.9
  Polyarthritis5/23.8
ANA+, n/%18/85.7
HLA-B27+, n/%2/9.5
RF+, n/%0/0
Age at JIA diagnosis, yrs (mean ± SD)3.7 ± 2.6
Age at uveitis diagnosis, yrs (mean ± SD)4.3 ± 3.2
Duration of uveitis, yrs (mean ± SD)7.5 ± 4.0
  • * Age at time of starting abatacept therapy. ANA: antinuclear antigen; RF: rheumatoid factor; ILAR: International League of Associations for Rheumatology; JIA: juvenile idiopathic arthritis.