Table 3A.

Laboratory findings in 23 patients with reported MAS for platelet count.

GroupPatient No.Event No.PLT, × 10 4/µlOutcome of MAS
Baseline ValueAt Time of MAS OnsetWorst Value During MASAt Time of Outcome
11137.312.76.223.8Recovered
2a240.623.14.140.6eRecovered
3321.611.911.925.1eRecovered
23421.68.33.329.5Recovered
4524.110.910.939Recovered
5614.49.49.445Recovered
714.414.411.427.5Recovered
6827.739332.3Recovered
7976.918.342.6eRecovered
81020.1101029.6Recovered
9b1140.6139.626.8Recovered
101213.18.53.915.5Recovered
111320.117.51624.9Recovered
121421.214.414.426.6Recovered
131569.318.20.27.1Not recovered
3141632.24.6d4.325.5Recovered
15c1731143.729.1Improved
Median24.112.99.427.5
Range13.1–76.94.6–390.2–18.37.1–45
4161831.57.1d7.120.7Recovered
171937.626.124.836.2Not recovered
182035.710.5d5.941eImproved
192112.71913.415.8Recovered
202225.113.912.724.2Recovered
212374.914.61.7Unknown
222425.82.7Recovered
2325Unknown
  • Baseline value: Value at start of TCZ administration in the all-patient registry surveillance.

  • a, b, c Representative examples of Group 1 (definitive MAS), Group 2 (probable MAS), and Group 3 (EB-VAHS), respectively.

  • d ± 1 day from onset.

  • e ± 3 days from outcome.