Table 1.

Frequency of SSc subgroups meeting the 2013 ACR/EULAR SSc criteria in comparison to previous criteria sets.

SSc Subgroup, n/N Tested (%)Total
PresclerodermalcSScdcSScSine SSc
ACR 1980 criteria, n/N tested (%)NA196/294 (67)97/97 (100)NA293/391 (75)
Medsger & Leroy criteria, n/N tested (%)24/24 (100)294/294 (100)NA10/10 (100)328/328 (100)
2013 ACR/EULAR criteria, n/N tested (%)18/24 (75)292/294 (99)97/97 (100)2/10 (20)409/425 (96)
  • SSc: systemic sclerosis; lcSSc: limited cutaneous systemic sclerosis; dcSSc: diffuse cutaneous systemic sclerosis; ACR: American College of Rheumatology; EULAR: European League Against Rheumatism; NA: not applicable.