Table 1.

Characteristics of 31 cases of macrophage activation syndrome.

CharacteristicNo. Cases (%)
Persistent fever31 (100)
Hepatosplenomegaly29 (93.55)
Enlarged lymph nodes20 (64.52)
Pancytopenia13 (41.94)
AST > 60 U/l24 (77.42)
Serum ferritin > 1500 ng/ml27 (87.10)
Fibrinogen < 2.5 g/l15 (48.39)
Triglyceride > 0.23 mmol/l23 (74.19)
LDH > 159 U/l27 (87.10)
Creatine kinase < 45 U/l31 (100)
Hemophagocytosis27 (87.10)
  • LDH: lactate dehydrogenase; AST: aspartate transaminase.