Table 1.

Clinical characteristics of dermatomyositis (DM) patients with anti-DFS70 antibodies in our cohort.

PatientSex/Age, yrsDiagnosisComplicationPrognosisSkin SymptomsElevation of CK*Anti-DFS70 Titer, U/mlDM Marker AutoantibodiesOther Autoantibodies
HGC
1F 25CADMSurviving++101.4MDA5p80-coilin8
2F 23CADMILDSurviving+++/−43.2MDA5
3F 46CADMILDDead+++/−29.7MDA5
4F 68Cancer-associated DMOvarian carcinomaDead+++28.0NXP-2
5M 1Juvenile DMSurviving+++50.4TIF1-γ
6F 6Juvenile DMAtopic dermatitisSurviving++30.2Unidentified
7F 46Classical DMSurviving++18.9
  • * Maximum elevation of creatine kinase (CK) is shown;

  • +: more than 1.5-fold of upper limit;

  • +/−: within 1.5-fold of upper limit;

  • −: within upper limit. H: heliotrope rash; G: Gottron’s sign; C: calcinosis; CADM: clinically amyopathic dermatomyositis; ILD: interstitial lung disease.