PHAPS, n = 13 | Controls, n = 50 | p | |
---|---|---|---|
Sex, women | 8 (61) | 40 (80) | 0.14 |
Mitral valve disease | 9 (75) | 11 (22) | 0.001 |
CNS disease | 8 (61) | 8 (16) | 0.001 |
Pregnancy morbidity* | 7 (87.5) | 13 (32.5) | 0.005 |
Skin involvement | 7 (54) | 4 (8) | 0.001 |
Pulmonary hypertension | 9 (75) | 5 (22) | 0.004 |
Low C3 | 1 (8) | 6 (18) | 0.65 |
Low C4 | 7 (54) | 13 (44) | 0.03 |
Lupus anticoagulant | 10 (91) | 38 (97) | 0.39 |
High β2-GPI IgG | 10 (83) | 8 (30) | < 0.001 |
High-titer aCL IgG | 12 (92) | 21 (43) | 0.002 |
↵* Percentage among women. PHAPS: pulmonary hemorrhage and antiphospholipid antibody syndrome; CNS: central nervous system; GPI: glycoprotein I; aCL: anticardiolipin; IgG: immunoglobulin.