Clinical Manifestation | Mi-2 (n = 4) | PM-Scl (n = 2) | U1RNP (n = 7) | Ku (n=l) | MJ (n = 16) | p155/140 (n = 14) |
---|---|---|---|---|---|---|
Sex F/M | 3/1 | 1/1 | 5/2 | 1/0 | 12/4 | 11/3 |
Diagnosis | ||||||
JPM | — | — | — | — | 2 | — |
JDM | 4 | 1 | 3 | — | 13 | 11 |
JOS | — | 1 | 4 | 1 | 1 | 3 |
Dysphagia | 2 | 1 | — | — | 5 | 3 |
Muscular | ||||||
Proximal weakness | 4 | 2 | 7 | 1 | 14 | 14 |
Contractures | — | 1 | 1 | — | 7 | 7 |
Atrophy | 4 | 1 | — | — | 7 | 2 |
DM cutaneous signs | 4 | — | 1 | — | 14 | 11 |
Cutaneous vasculitis | — | 1 | 1 | — | 6 | 8 |
Calcinosis | 1 | — | — | — | 5 | 5 |
Interstitial lung disease | — | 1 | 2 | — | 4 | 1 |
Arthritis | 1 | 1 | 3 | — | 6 | 9 |
Raynaud phenomenon | — | 2 | 3 | — | 1 | 4 |
JOS: juvenile overlap syndrome; JPM: juvenile polymyositis; JDM: juvenile dermatomyositis.