Survival rates in studies of idiopathic inflammatory myopathies (IIM). Survival percentages of IIM in references 6, 11, and 12 and that of primary DM in reference 10 were calculated from Kaplan-Meier curves in the reports.
| Study | No. Patients, Source (Study Period) | Survival Percentages of IIM at 5/10 Yrs, Unless Otherwise Specified (No.) | Remarks | |||||
|---|---|---|---|---|---|---|---|---|
| ADM | DM | PM | JIM | OM | CAM | |||
| Medsger2, USA, 1971 | 124, clinics in the region (1947–68) | NI | 72/53 at 2/7 yrs (86 adult-onset PM/DM, 24 JIM, 7 OM, 6 CAM) | First described life-table analysis in IIM | ||||
| Benbassat3, Israel, 1985 | 92, population-based (1956–76) | NI | 15.2** (29) | 13.3** (18) | 11.5** (20) | 18.6** (12) | 44.0** (13) | |
| Hochberg31, USA, 1986 | 76, single institute (1970–81) | NI | 78.2* (21) | 63.1* (31) | NI | 72.8* (18) | 80.0* (6) | |
| Maugars6, France, 1996 | 69, single institute (1973–94) | NI | 59/ND (27) | 77/ND (13) | 90/ND (10) | 80/ND (10) | 34/ND (9) | |
| Marie7, France 2001 | 77, 2 institutes (1983–98) | NI | 82/61 at 5/15 yrs (36 DM and 41 PM including 11 CAM) | NI | Included in PM/DM | |||
| Sultan8, UK, 2001 | 46, single institute (1978–99) | NI | 95/84 (23 PM, 14 DM, 1 JIM, 8 OM) | NI | 4 DM included with normal CK levels | |||
| Danko9, Hungary, 2004 | 162, single institute (1976–2001) | NI | 94/84 (42) | 90/86 (75) | 100/100 (9) | 96/96 (29) | 71/71 (7) | PM vs DM, NSa |
| Airio10, Finland, 2006 | 248, population-based (1969–85) | NI | 75/55 (72) | 63/53 (176) | NI | NI | PM vs DM, NSa; 5/10-year survival of DM was 87/67% if 22 CAM were excluded | |
| Torres11, Spain, 2006 | 107, single institute, (1976–2005) | NI | 97/87 (30) | 76/70 (22) | 84/84 (21) | 95/ND (15) | 58/50 (19) | PM vs DM, NSa |
| Kameda12, Japan, 2006 | 110, single institute, (1985–2002) | 58/ND (14) | 69/ND (32) | 78/ND (18) | NI | 85/ND (33) | 0/0 (13) | |
| Yamasaki, Japan, 2011 | 197, single institute (1984–2009) | 61/61 (21) | 77/64 (74) | 91/87 (43) | NI | 88/79 (38) | 25/25 (21) | PM > DM, p = 0.0427b |
↵* Percent survival at 8 years.
↵** Mortality per 100 person-years.
↵a No statistical difference of survival between primary DM and primary PM.
↵b Primary DM had lower survival compared to primary PM. IIM: idiopathic inflammatory myopathies; ADM: amyopathic dermatomyositis; DM: dermatomyositis; PM: polymyositis; JIM: juvenile inflammatory myopathies; OM: overlap myositis; CAM: cancer-associated myositis; NI: not included; ND: no data; NS: not significant.