Table 1.

Causes of PR3-specific c-ANCA other than Wegener’s granulomatosis.

Connective tissue disease
Cocaine-induced midline destructive lesions
Subacute bacterial endocarditis
Tuberculosis
Chronic hepatitis B virus infection
Chronic hepatitis C virus infection
Amoebic liver abscess
Phlegmon
Cystic fibrosis
Ventriculoperitoneal shunt nephritis
Parvovirus B19
  • PR3: proteinase 3; c-ANCA: cytoplasmic antineutrophil cytoplasmic antigen.