PT  - JOURNAL ARTICLE
AU  - Alexandre Terré
AU  - Alexis Talbot
AU  - Camille Louvrier
AU  - Jean Baptiste  Picque
AU  - Matthieu Mahévas
AU  - David Boutboul
AU  - Serge Amselem
AU  - Irina Giurgea
AU  - Gilles Grateau
AU  - Sophie Georgin-Lavialle
TI  - Monoclonal Gammopathy, Arthralgias, and Recurrent Fever Syndrome: A New Autoinflammatory Syndrome?
AID  - 10.3899/jrheum.181204
DP  - 2019 Mar 15
TA  - The Journal of Rheumatology
PG  - jrheum.181204
4099  - http://www.jrheum.org/content/early/2019/08/08/jrheum.181204.short
4100  - http://www.jrheum.org/content/early/2019/08/08/jrheum.181204.full
AB  - Objective To describe a new autoinflammatory syndrome with recurrent fever and monoclonal gammopathy that differs from Schnitzler syndrome. Methods We conducted a retrospective study of patients with monoclonal gammopathy and recurrent fever of unknown origin. Results Five patients were studied; median age at onset of symptoms was 44 years. Median frequency of fever attacks was 6 episodes per year. In the absence of treatment, the median duration of fevers was 3 days. Conclusion This new autoinflammatory syndrome is defined by an association among monoclonal gammopathy, arthralgias, and recurrent fever.