RT Journal Article
SR Electronic
T1 Monoclonal gammopathy, arthralgias, and recurrent fever syndrome: a new autoinflammatory syndrome?
JF The Journal of Rheumatology
JO J Rheumatol
FD The Journal of Rheumatology
SP jrheum.181204
DO 10.3899/jrheum.181204
A1 Alexandre Terré
A1 Alexis Talbot
A1 Camille Louvrier
A1 Jean Baptiste  Picque
A1 Matthieu Mahévas
A1 Serge Amselem
A1 Irina Giurgea
A1 David Boutboul
A1 Gilles Grateau
A1 Sophie Georgin  Lavialle
YR 2019
UL http://www.jrheum.org/content/early/2019/03/11/jrheum.181204.abstract
AB Objective The objective of this work was to describe a new autoinflammatory syndrome with recurrent fever and monoclonal gammopathy that differs from Schnitzler syndrome. Methods We conducted a retrospective study of patients with monoclonal gammopathy and recurrent fever of unknown origin. Results Five patients were included in the description. The median age at onset of symptoms was 44 years old. The median frequency of fever attacks was 6 episodes per year. In the absence of treatment, the median duration of fevers was 3 days. Conclusion This new autoinflammatory syndrome is defined by an association between monoclonal gammopathy, arthralgias, and recurrent fever (MGARF).