PT - JOURNAL ARTICLE AU - Elaine S. Xie AU - Nikhil Pai AU - Michelle Batthish TI - Limited GPA and Alpha-1 Antitrypsin Deficiency in a Pediatric Patient AID - 10.3899/jrheum.180979 DP - 2019 Mar 01 TA - The Journal of Rheumatology PG - jrheum.180979 4099 - http://www.jrheum.org/content/early/2019/02/25/jrheum.180979.short 4100 - http://www.jrheum.org/content/early/2019/02/25/jrheum.180979.full AB - Granulomatosis with polyangiitis (GPA) is a rare systemic vasculitis affecting small to medium-sized blood vessels. The most frequent presenting symptoms are nonspecific constitutional symptoms, followed by pulmonary, renal, and upper respiratory tract symptoms1