RT Journal Article SR Electronic T1 Cutaneous mastocytosis in a patient with primary Sjögren's syndrome. JF The Journal of Rheumatology JO J Rheumatol FD The Journal of Rheumatology SP 1697 OP 1700 VO 33 IS 8 A1 Shebnem Kalay Erbay A1 Carol Stewart A1 Ashraf Hassanein A1 Andrew Fletcher A1 Indraneel Bhattacharyya A1 Donald Cohen A1 Stanton K Wesson A1 Jason Weinstein A1 Robert Lyons A1 Westley H Reeves YR 2006 UL http://www.jrheum.org/content/33/8/1697.abstract AB Mast cells have been linked to rheumatoid arthritis (RA) and are essential to the pathogenesis of RA-like disease in a mouse model. We describe a 34-year-old woman who developed Sjögren's syndrome concurrently with telangiectasia macularis eruptiva perstans (TMEP), a rare form of cutaneous mastocytosis. The patient had sicca symptoms with an abnormal minor salivary gland biopsy and decreased salivary flow, peripheral neuropathy, an 80 pound weight loss, and a macular erythematous rash that exhibited superficial perivascular mast cell infiltrates on biopsy of lesional skin. This case further underscores the link between mast cells and the development of autoimmunity.