Spinal cord involvement has been observed rarely in primary central nervous system vasculitis (PCNSV), and histopathologically proven isolated cord angiitis usually involves the thoracic level or terminal conus1,2. We report a very rare case of isolated cervical cord involvement in PCNSV. The diagnosis was first made by spinal magnetic resonance imaging (MRI) to survey the possible etiologies of cervical myelopathy, and finally confirmed …